BCOR
BCL6 corepressor
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co-repressor that potentiates transcriptional repression by BCL-6 [Pubmed]; counteracts the oncogenic active NOTCH to restrain transformation in T-ALL [Pubmed]
This census gene has a hallmark. For more information please look
[here].
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role in cancer | TSG, fusion |
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global regulation of gene expression | the BCOR complex contains Polycomb group proteins, including a histone H2A ubiquitin E3 ligase, an SCF ubiquitin E3 ligase, and a JmjC domain histone H3 K36 demethylase, which through epigenetic modifications of chromatin, enable silencing of BCL6 targets [Pubmed] |
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differentiation and development | required for vertebrate laterality determination [Pubmed]; helps control myeloid cell differentiation [Pubmed] |
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types of alteration in cancer | internal tandem duplications (ITDs) involving exon 15 in high-grade uterine sarcoma [Pubmed] |
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impact of mutation on function | deletion of exon 4 results in Myc hyperactivation and induces leukaemic transformation in T-ALL [Pubmed] |
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fusion partner | RARA in APL [Pubmed]; ZC3H7B in endometrial stromal sarcoma [Pubmed]; CCNB3 in undifferentiated sarcomas of male children [Pubmed]; MAML3 in undifferentiated small blue round cell sarcoma [Pubmed] |
suppression of growth
LOF mutations result in increased proliferation, while overexpression impairs proliferation in bone marrow cells [Pubmed]